CC BY 4.0 · Aorta (Stamford) 2019; 07(06): 169-171
DOI: 10.1055/s-0039-3401809
Case Report
Thieme Medical Publishers 333 Seventh Avenue, New York, NY 10001, USA.

Primary Sarcoma of Descending Aorta

1   Department of Thoracic Surgery, IEO, European Institute of Oncology IRCSS, Milan, Italy
,
Alessio V. Mariolo
1   Department of Thoracic Surgery, IEO, European Institute of Oncology IRCSS, Milan, Italy
,
1   Department of Thoracic Surgery, IEO, European Institute of Oncology IRCSS, Milan, Italy
,
1   Department of Thoracic Surgery, IEO, European Institute of Oncology IRCSS, Milan, Italy
,
Rosa Spirito
2   Department of Cardiovascular Surgery of the University of Milan, Centro Cardiologico Monzino IRCSS, Milan, Italy
,
Lorenzo Spaggiari
1   Department of Thoracic Surgery, IEO, European Institute of Oncology IRCSS, Milan, Italy
3   Department of Oncology and Hemato-Oncology, University of Milan, Milan, Italy
› Author Affiliations
Funding None.
Further Information

Publication History

18 December 2018

02 November 2019

Publication Date:
09 April 2020 (online)

Abstract

Primitive aortic sarcomas are rare tumors characterized by resistance to medical treatment and a poor prognosis with high metastatic rates and local recurrences. Surgery remains the mainstay treatment and is based on challenging and technically demanding resections with high rate of major intraoperative and postoperative complications. We report the case of a patient with primitive intimal sarcoma of the aorta, who underwent a descending aortic resection and reconstruction with a prosthetic tube.

 
  • References

  • 1 Kato W, Usui A, Oshima H, Suzuki C, Kato K, Ueda Y. Primary aortic intimal sarcoma. Gen Thorac Cardiovasc Surg 2008; 56 (05) 236-238
  • 2 Dedeilias P, Koletsis E, Nenekidis I. , et al. Intimal aortic sarcoma mimicking ruptured thoracoabdominal type IV aneurysm. A rare case report and review of the literature. J Cardiothorac Surg 2011; 6: 162
  • 3 Sebenik M, Ricci Jr A, DiPasquale B. , et al. Undifferentiated intimal sarcoma of large systemic blood vessels: report of 14 cases with immunohistochemical profile and review of the literature. Am J Surg Pathol 2005; 29 (09) 1184-1193
  • 4 Chiche L, Mongrédien B, Brocheriou I, Kieffer E. Primary tumors of the thoracoabdominal aorta: surgical treatment of 5 patients and review of the literature. Ann Vasc Surg 2003; 17 (04) 354-364
  • 5 Sugiura J, Oshima H, Abe T. , et al. The efficacy and risk of cerebrospinal fluid drainage for thoracoabdominal aortic aneurysm repair: a retrospective observational comparison between drainage and non-drainage. Interact Cardiovasc Thorac Surg 2017; 24 (04) 609-614