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CC BY-NC-ND 4.0 · Journal of Health and Allied Sciences NU 2013; 03(01): 76-78
DOI: 10.1055/s-0040-1703640
Case Report

XERODERMA PIGMENTOSA WITH MULTIPLE CUTANEOUS MALIGNANCIES– A RARE CASE REPORT AND REVIEW OF LITERATURE

Rohan Shetty
1   Assistant Professor, Department of Surgery, K. S. Hedge Medical Academy, Nitte University, Deralakatte, Mangalore - 575 018
,
Girish B. S.
2   Associate Professor, Department of Dermatology, K. S. Hedge Medical Academy, Nitte University, Deralakatte, Mangalore - 575 018
,
Rajesh Ballal
3   Professor, Department of Surgery, K. S. Hedge Medical Academy, Nitte University, Deralakatte, Mangalore - 575 018
,
Harish S. Permi
4   Associate Professor, Department of Pathology, K. S. Hedge Medical Academy, Nitte University, Deralakatte, Mangalore - 575 018
,
Pramodh Makannavar
5   Post graduate, Department of Surgery, K. S. Hedge Medical Academy, Nitte University, Deralakatte, Mangalore - 575 018
,
Vinay Alva
6   Post graduate, Department of Surgery, K. S. Hedge Medical Academy, Nitte University, Deralakatte, Mangalore - 575 018
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Abstract

Xeroderma pigmentosa is a rare autosomal recessive disorder, characterized by photosensitivity, pigmentary changes, premature skin aging, and marked increase in risk of developing malignant neoplasms of the skin and eyes. Here we present a 13 year old girl with xeroderma pigmentosa who developed multiple cutaneous malignancies in the face and upper limb.

Keywords

Xeroderma pigmentosa - multiple skin cancer - squamous cell carcinoma - basal cell carcinoma


Publication History

Article published online:
27 June 2020

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