Download PDF
CC BY-NC-ND 4.0 · Rev Bras Ortop (Sao Paulo) 2023; 58(03): 532-537
DOI: 10.1055/s-0040-1716757
Relato de Caso
Mão

Fracture in Humeroradial Synostosis: Description of Two Clinical Cases[*]

Article in several languages: português | English
Ricardo Kaempf de Oliveira
1   Grupo de Cirurgia de Mão, Santa Casa de Misericórdia de Porto Alegre, Porto Alegre, RS, Brasil
2   Hospital Mãe de Deus de Porto Alegre, Porto Alegre, RS, Brasil
,
João Pedro Farina Brunelli 
3   Hospital Santa Casa de São Paulo, São Paulo, SP, Brasil
,
Márcio Aurelio Aita 
4   Faculdade de Medicina do ABC, Santo André, SP, Brasil
,
Pedro José Delgado Serrano
5   Unidade de Cirurgia de Mão, Hospital Universitário Madrid Montepríncipe, Universidade CEU San Pablo, Boadilla del Monte, Madri, Espanha
› Author Affiliations Financial Support The present study did not receive any financial support from either public, commercial or not-for-profit sources.
› Further Information
   Permissions and Reprints

Abstract

Synostosis is a generic term to indicate the union of two originally separated bones. At the elbow, humeroradial or longitudinal synostosis causes significant disability, which varies depending on hand function, elbow positioning, adjacent joints mobility and contralateral limb function. It is estimated that, to date, a little more than 150 patients have been described with this deformity, which is more common in subjects with deficient ulnar formation or affected by conditions such as Antley-Bixler and Hermann syndromes. The lack of the elbow joint, with the formation of a longer bone due to humerus-radius fusion, results in stiffness. As such, it is assumed that fractures in this topography are not uncommon. However, since synostosis is rare, this lesion was only described twice in the literature. We report two patients with a fracture of the single bone formed by a humeroradial synostosis and Bayne type-IV ulnar formation failure. Both patients were treated surgically with success. We emphasize the need for adequate treatment to not compromise the daily activities of patients who are adapted to their deformity, thus avoiding worsening the function of a previously affected limb.

Keywords

synostosis/surgery - radius/abnormalities - congenital abnormalities - syndrome - ulna/abnormalities.

* Study developed at Hospital Santa Casa de Porto Alegre and Hospital Mãe de Deus, Porto Alegre, Brazil.




Publication History

Received: 20 April 2020

Accepted: 06 July 2020

Article published online:
18 December 2020

© 2020. Sociedade Brasileira de Ortopedia e Traumatologia. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/)

Thieme Revinter Publicações Ltda.
Rua do Matoso 170, Rio de Janeiro, RJ, CEP 20270-135, Brazil

 

  • Referências

  • 1 Kozin SH. Congenital differences about the elbow. Hand Clin 2009; 25 (02) 277-291
    CrossrefPubMedGoogle Scholar
  • 2 McCall AA, Kirsch CF, Ishiyama G, Ishiyama A. Otologic findings in Antley-Bixler syndrome: a clinical and radiologic case report. Int J Pediatr Otorhinolaryngol 2007; 71 (07) 1139-1143
    CrossrefPubMedGoogle Scholar
  • 3 Hosalkar HS, Shah HS, Gujar PS, Shaw BA. The Antley-Bixler syndrome: two new cases. J Postgrad Med 2001; 47 (04) 252-255
    PubMedGoogle Scholar
  • 4 Tabrizi A, Afshar A, Aidenlou A. A case of failure to correct humerus-radius synostosis and thumb hypoplasia. J Hand Surg Eur Vol 2018; 43 (02) 211-213
    CrossrefPubMedGoogle Scholar
  • 5 McIntyre JD, Brooks A, Benson MK. Humeroradial synostosis and the multiple synostosis syndrome: case report. J Pediatr Orthop B 2003; 12 (03) 192-196
    PubMedGoogle Scholar
  • 6 Nema S, Vyas G, Sirsikar A, Bhoj PK. Congenital humeroradial synostosis: a case report. Malays Orthop J 2012; 6 (SupplA): 41-42 DOI: 10.5704/MOJ.1211.010.
    CrossrefPubMedGoogle Scholar
  • 7 Pfeiffer RA, Braun-Quentin C. Genetic nosology and counseling of humeroradial synostosis. Genet Couns 1994; 5 (03) 269-274
    PubMedGoogle Scholar
  • 8 Miller JK, Wenner SM, Kruger LM. Ulnar deficiency. J Hand Surg Am 1986; 11 (06) 822-829
    CrossrefPubMedGoogle Scholar
  • 9 Swanson AB, Tada K, Yonenobu K. Ulnar ray deficiency: its various manifestations. J Hand Surg Am 1984; 9 (05) 658-664
    CrossrefPubMedGoogle Scholar
  • 10 Cole RJ, Manske PR. Classification of ulnar deficiency according to the thumb and first web. J Hand Surg Am 1997; 22 (03) 479-488
    CrossrefPubMedGoogle Scholar
  • 11 Card RY, Strachman J. Congenital ankylosis of the elbow. J Pediatr 1955; 46 (01) 81-85
    CrossrefPubMedGoogle Scholar