J Neurol Surg A Cent Eur Neurosurg 2022; 83(03): 294-297
DOI: 10.1055/s-0041-1722969
Case Report

Epithelioid Hemangioendothelioma in the Area of the Neurovascular Bundle of the Upper Arm Mimicking a Schwannoma of the Ulnar Nerve

Christian Scheller
1   Department of Neurosurgery, University of Halle-Wittenberg, Sachsen-Anhalt, Germany
,
Stefan Rampp
1   Department of Neurosurgery, University of Halle-Wittenberg, Sachsen-Anhalt, Germany
,
Julian Prell
2   Department of Neurosurgery, University Hospital Halle (Saale), Halle (Saale), Germany
,
Christian Strauss
1   Department of Neurosurgery, University of Halle-Wittenberg, Sachsen-Anhalt, Germany
,
Endres John
1   Department of Neurosurgery, University of Halle-Wittenberg, Sachsen-Anhalt, Germany
,
Ukkat Jörg
3   Department of General Surgery, University of Halle-Wittenberg, Halle (Saale), Sachsen-Anhalt, Germany
,
Linda Diessel
4   Department of Pathology, University of Halle-Wittenberg, Halle (Saale), Sachsen-Anhalt, Germany
,
Silvio Brandt
5   Department of Neuroradiology, University of Halle-Wittenberg, Halle (Saale), Sachsen-Anhalt, Germany
,
Tobias Müller
6   Department of Neurology, University of Halle-Wittenberg, Halle (Saale), Sachsen-Anhalt, Germany
› Author Affiliations

Abstract

Epithelioid hemangioendothelioma (EH) is a rare vascular malignant sarcoma. To date, there are only two published case reports of EH mimicking nerve sheath tumors of a peripheral nerve. A 41-year-old woman presented with a painful node on the inside of the upper arm and motor deficits of the ulnar nerve. Magnetic resonance imaging (MRI) follow-up and neurosonography revealed a slowly progressive, contrast-enhancing tumor in the area of the neurovascular bundle. A schwannoma of the ulnar nerve was suspected. At surgery, the tumor was adherent to the brachial artery, but not to nerves. Pathology revealed an EH. EH may mimic a nerve sheath tumor and should be taken into consideration, especially because of its potential for metastasis and fatal progression.

Patient Consent

The patient has consented to the submission of the case report for submission to the journal.




Publication History

Received: 23 June 2020

Accepted: 22 September 2020

Article published online:
12 April 2021

© 2021. Thieme. All rights reserved.

Georg Thieme Verlag KG
Rüdigerstraße 14, 70469 Stuttgart, Germany