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CC BY-NC-ND 4.0 · Indian Journal of Neurosurgery 2021; 10(02): 169-172
DOI: 10.1055/s-0041-1725208
Case Report

Lhermitte–Duclos Disease Mimicking Cerebellopontine Angle Tumor: A Case Report

Bilal Abbasoglu 
1   Medical Faculty Brain and Nerve Surgery Department, Ankara University, Ankara, Turkey
,
Murat Zaimoglu 
1   Medical Faculty Brain and Nerve Surgery Department, Ankara University, Ankara, Turkey
,
Umit Eroglu 
1   Medical Faculty Brain and Nerve Surgery Department, Ankara University, Ankara, Turkey
,
Cevriye Cansiz Ersoz 
2   Medical Faculty Pathology Department, Ankara University, Ankara, Turkey
,
Ayhan Attar
1   Medical Faculty Brain and Nerve Surgery Department, Ankara University, Ankara, Turkey
› Author Affiliations Funding The pathological sections and images included in the present case study are supported by the Scientific Research Project (14A0230003).
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Abstract

Lhermitte-Duclos disease (LDD) is dysplastic gangliocytoma of the cerebellum, which is rare, tends to grow slowly, usually has good prognosis, and wherein the cerebellar cortex becomes thick and the central white matter is not observed. On MRI of the brain, it has hyperintense and hypointense presentations on T2- and T1-weighted scans, respectively. It has nonhomogenous contrasting pattern on T1-contrast scans. LDD can be seen unilaterally or bilaterally in the cerebellum. When the disease is located at the cerebellopontine angle, it can be mistaken for the tumors located in this region. Recurrence can occur postoperatively, which is rare. The present case is a rare one because the tumor was located at the cerebellopontine angle and radiologically mimicked cerebellopontine angle tumors.

Keywords

Cerebellopontine angle - Cerebellar gangliocytoma - Lhermitte–Duclos disease


Publication History

Article published online:
15 July 2021

© 2021. Neurological Surgeons’ Society of India. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial-License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/).

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