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CC BY-NC-ND 4.0 · Thorac Cardiovasc Surg Rep 2021; 10(01): e49-e51
DOI: 10.1055/s-0041-1728720
Case Report: Cardiac

Mitral Annular Calcification in Marfan Syndrome: A 38-Year Follow-Up Observation

Kazutaka Horiuchi
1   Department of Cardiovascular Surgery, Okazaki City Hospital, Okazaki, Aichi, Japan
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Abstract

Background Mitral annular calcification (MAC) associated with Marfan syndrome is rare in comparison with that frequently found in elderlies with valvular disease.

Case Presentation A 17-year-old woman with Marfan syndrome underwent mitral valve replacement for severe mitral regurgitation. Preoperative examination showed mitral valve prolapse and a dense C -shaped MAC. We evaluated MAC and adjacent area, respectively, in postoperative 18 and 38 years, and neither progression nor expansion of calcification was observed.

Conclusion MAC associated with Marfan syndrome is more likely to be caused by stresses due to valve prolapse than by connective tissue disorder.

Keywords

mitral annular calcification - Marfan syndrome - mitral valve prolapse


Publication History

Received: 29 December 2020

Accepted: 22 February 2021

Article published online:
28 August 2021

© 2021. The Author(s). This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/)

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