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DOI: 10.1055/s-0041-1729136
Lhermitte–Duclos Disease: Incidental Finding in Traumatic Cerebral Hemorrhage
Funding None.
Abstract
Lhermitte–Duclos disease, also known as dysplastic cerebellar gangliocytoma, is a rare hamartomatous tumor localized in cerebellum. An association with Cowden syndrome is observed in 50% of cases who present with symptoms of increased intracranial pressure and cerebellar ataxia. These patients have specific magnetic resonance imaging and histopathological findings. Surgical resection is the treatment of choice. Here, we report a case of a young female with traumatic frontal hemorrhage associated with Lhermitte–Duclos disease.
Publication History
Article published online:
07 July 2021
© 2021. Neurotrauma Society of India. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial-License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/).
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References
- 1
Louis DN,
Ohgaki H,
Wiestler OD.
et al
The 2007 WHO classification of tumours of the central nervous system. Acta Neuropathol
2007; 114 (02) 97-109
MissingFormLabel
- 2 Pandey S, Sarma N. Lhermitte-Duclos disease: a rare cause of cerebellar ataxia. Asian J Neurosurg 2017; 12 (04) 705-706
- 3 Nowak DA, Trost HA, Porr A, Stölzle A, Lumenta CB. Lhermitte-Duclos disease (Dysplastic gangliocytoma of the cerebellum). Clin Neurol Neurosurg 2001; 103 (02) 105-110
- 4 Robinson S, Cohen AR. Cowden disease and Lhermitte-Duclos disease: characterization of a new phakomatosis. Neurosurgery 2000; 46 (02) 371-383
- 5 Nowak DA, Trost HA. Lhermitte-Duclos disease (dysplastic cerebellar gangliocytoma): a malformation, hamartoma or neoplasm. ? Acta Neurol Scand 2002; 105 (03) 137-145
- 6 Milbouw G, Born JD, Martin D. et al Clinical and radiological aspects of dysplastic gangliocytoma (Lhermitte-Duclos disease): a report of two cases with review of the literature. Neurosurgery 1988; 22 (01) 124-128
- 7 Meltzer CC, Smirniotopoulos JG, Jones RV. The striated cerebellum: an MR imaging sign in Lhermitte-Duclos disease (dysplastic gangliocytoma). Radiology 1995; 194 (03) 699-703
- 8 Borni M, Kammoun B, Kolsi F, Abdelmouleh S, Boudawara MZ. The Lhermitte-Duclos disease: a rare bilateral cerebellar location of a rare pathology. Pan Afr Med J 2019; 33: 118
- 9 Bozbuga M, Gulec I, Suslu HT, Bayindir C. Bilateral Lhermitte-Duclos disease. Neurol India 2010; 58 (02) 309-311