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CC BY 4.0 · Aorta (Stamford) 2021; 09(04): 165-166
DOI: 10.1055/s-0041-1729916
Images in Aortic Disease

Black Aorta from Alkaptonuria

James P. Laurent
1   Department of Cardiothoracic Surgery, Wellington Regional Hospital, Wellington, New Zealand
,
Sean D. Galvin
1   Department of Cardiothoracic Surgery, Wellington Regional Hospital, Wellington, New Zealand
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Abstract

A-76-year old male with a past history of alkaptonuria with ochronosis (homogentisic acid deposition in tissues) had symptomatic aortic stenosis. Surgical replacement of the valve was undertaken, and he was noted to have a severely pigmented and porcelain aorta.

Keywords

aorta - alkaptonuria - ochronosis - aortic valve replacement


Publication History

Received: 07 August 2020

Accepted: 26 February 2021

Article published online:
29 October 2021

© 2021. The Author(s). This is an open access article published by Thieme under the terms of the Creative Commons Attribution License, permitting unrestricted use, distribution, and reproduction so long as the original work is properly cited. (https://creativecommons.org/licenses/by/4.0/)

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