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CC BY-NC-ND 4.0 · Indian J Radiol Imaging 2021; 31(03): 689-692
DOI: 10.1055/s-0041-1736165
Case Report

An Unusual Cause of Cholestasis in an Infant: Biliary Atresia Type IIB

Poonam Sherwani
1   Department of Radiodiagnosis, All India Institute of Medical Sciences, Rishikesh, Uttarakhand, India
,
Rishi Bolia
2   Department of Pediatrics, All India Institute of Medical Sciences, Rishikesh, Uttarakhand, India
,
Ashish Kaushik
1   Department of Radiodiagnosis, All India Institute of Medical Sciences, Rishikesh, Uttarakhand, India
,
Sumit Kumar
1   Department of Radiodiagnosis, All India Institute of Medical Sciences, Rishikesh, Uttarakhand, India
,
Sanjeev Kishore
3   Department of Pathology, All India Institute of Medical Sciences, Rishikesh, Uttarakhand, India
,
Udit Chauhan
1   Department of Radiodiagnosis, All India Institute of Medical Sciences, Rishikesh, Uttarakhand, India
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Abstract

Biliary atresia (BA) is a progressive destructive cholangiopathy of unknown etiology that presents in early infancy. It has a worldwide frequency of 1:8,000–1:15,000 and is common in Asia than in the west. Based on the level at which the lumen of the extrahepatic duct is obliterated, BA is classified into three types. Type III is the commonest (∼85%) type and has the most proximal level of obstruction in the porta hepatis, while type II in which the atresia is at the level of the common hepatic duct, is the least common (∼2.5%) and has been rarely reported. Here, we report the imaging features of an infant with type IIB biliary atresia.

Keywords

biliary atresia - cholangiopathy - common hepatic duct


Publication History

Article published online:
06 October 2021

© 2021. Indian Radiological Association. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/)

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