CC BY-NC-ND 4.0 · Thorac Cardiovasc Surg Rep 2022; 11(01): e20-e22
DOI: 10.1055/s-0042-1742781
Case Report: Thoracic

Extrapleural Pneumonectomy for Sarcoma of the Lung in a Pediatric Patient

1   Department of Surgery, University Hospital Schleswig-Holstein, Luebeck, Germany
Ana B. Almeida
1   Department of Surgery, University Hospital Schleswig-Holstein, Luebeck, Germany
Jessica Pablik
2   Department of Pathology, University Hospital, Dresden, Germany
› Author Affiliations


Pediatric sarcomas are rare entities. Bone sarcomas and rhabdomyosarcoma are most common, whereas primary sarcoma of the lung is extremely uncommon. Pneumonectomy is only very infrequently performed in the pediatric population. We report on a 16-year-old girl with an undifferentiated high-grade pleomorphic sarcoma of the left lung. There was no comorbidity and no history of previous malignant disease. The huge tumor originated from the left lower lobe and had spread to the left pleura. As part of a multimodal approach, she underwent extrapleural pneumonectomy with en bloc resection of the pleura, lung, pericardium, and diaphragm.


This study was presented at the 29th European Conference on General Thoracic Surgery, June 20–22, 2021 (Virtual ESTS Meeting).

Publication History

Received: 07 July 2021

Accepted: 18 November 2021

Article published online:
03 March 2022

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