Semin Respir Crit Care Med 2022; 43(06): 792-808
DOI: 10.1055/s-0042-1755565
Review Article

High-Resolution Computed Tomography of Cystic Lung Disease

Joanna E. Kusmirek
1   Department of Radiology, University of Wisconsin School of Medicine and Public Health, Madison, Wisconsin
,
Cristopher A. Meyer
1   Department of Radiology, University of Wisconsin School of Medicine and Public Health, Madison, Wisconsin
› Institutsangaben

Abstract

The cystic lung diseases (CLD) are characterized by the presence of multiple, thin-walled, air-filled spaces in the pulmonary parenchyma. Cyst formation may occur with congenital, autoimmune, inflammatory, infectious, or neoplastic processes. Recognition of cyst mimics such as emphysema and bronchiectasis is important to prevent diagnostic confusion and unnecessary evaluation. Chest CT can be diagnostic or may guide the workup based on cyst number, distribution, morphology, and associated lung, and extrapulmonary findings. Diffuse CLD (DCLDs) are often considered those presenting with 10 or more cysts. The more commonly encountered DCLDs include lymphangioleiomyomatosis, pulmonary Langerhans' cell histiocytosis, lymphoid interstitial pneumonia, Birt–Hogg–Dubé syndrome, and amyloidosis/light chain deposition disease.



Publikationsverlauf

Artikel online veröffentlicht:
17. Oktober 2022

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