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CC BY 4.0 · Rev Bras Ortop (Sao Paulo) 2024; 59(S 01): e104-e108
DOI: 10.1055/s-0043-1771005
Relato de Caso

Painless Growing Swelling on the Palm of a 4-year-old Boy: Malignant Peripheral Nerve Sheath Tumor

Article in several languages: português | English
Recep Öztürk 
1   Hospital de Treinamento e Pesquisa em Oncologia Dr. Abdurrahman Yurtaslan Ankara, Departamento de Ortopedia e Traumatologia, Ancara, Turquia
,
Kemal Kösemehmetoğlu
2   Universidade Hacettepe, Faculdade de Medicina, Departamento de Patologia, Ancara, Turquia
,
Fisun Ardıç Yükrük
3   Hospital de Treinamento e Pesquisa em Oncologia Dr. Abdurrahman Yurtaslan Ankara, Departamento de Patologia, Ancara, Turquia
,
Bedii Şafak Güngör
1   Hospital de Treinamento e Pesquisa em Oncologia Dr. Abdurrahman Yurtaslan Ankara, Departamento de Ortopedia e Traumatologia, Ancara, Turquia
› Author Affiliations Financial Support The present study received no financial support from public, commercial, or not-for-profit sources.
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Abstract

In this study, we present a 4-year-old male patient with a slowly growing painless mass in the palm of his left hand for 2 years. Although musculoskeletal tumors are rare, hand localized tumors are even rarer in pediatric patients. The fact that very few (less than one in ten) tumors are malignant and there are dozens of subtypes, each with different treatment management, shows the importance of the management of these lesions. Appropriate diagnosis and management of soft tissue masses, especially insidious malignant tumors, is vital. Due to the rarity of soft tissue tumors, adequate guidelines for their management are limited. The purpose of this report is to present an example of the approach to one of the soft tissue tumors.

Keywords

child - diagnosis, differential - sarcoma - soft tissue neoplasms

Note

This study is a case report and is exempt from ethics committee approval in our country. Written informed consent was obtained from the patient’s guardian.


Study carried out at the Department of Orthopaedics, Dr. Abdurrahman Yurtaslan Ankara Oncology Training and Research Hospital, Ankara, Turkey.




Publication History

Received: 26 July 2022

Accepted: 16 December 2022

Article published online:
24 October 2023

© 2023. The Author(s). This is an open access article published by Thieme under the terms of the Creative Commons Attribution 4.0 International License, permitting copying and reproduction so long as the original work is given appropriate credit (https://creativecommons.org/licenses/by/4.0/)

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