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Geburtshilfe Frauenheilkd 2018; 78(04): 345-348
DOI: 10.1055/s-0044-100781
GebFra Magazin
Der interessante Fall
Georg Thieme Verlag KG Stuttgart · New York

Ein seltener Fall einer jungen Patientin mit Herlyn-Werner-Wunderlich-Syndrom nach der Menarche

Philipp Meyer-Wilmes
,
Sebastian Daniel Schäfer
,
Ludwig Kiesel
,
Felix Strube
Further Information

Publication History

Publication Date:
27 April 2018 (online)

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Das Herlyn-Werner-Wunderlich-Syndrom (HWWS) gehört zu den seltenen Entwicklungsanomalien der weiblichen Geschlechtsorgane. Hierbei liegt ein Uterus didelphys mit einseitig obstruierter Hemivagina und einer ipsilateralen Nierenagenesie vor. Wir präsentieren den Fall einer jungen Patientin, die sich mit zyklischen Unterbauchschmerzen und dem Verdacht auf ein Hämatokolpos in unserer gynäkologischen Sprechstunde vorstellte.
 

  • Literatur

  • 1 Rock JA, Jones jr. HW. The double uterus associated with an obstructed hemivagina and ipsilateral renal agenesis. Am J Obstet Gynecol 1980; 138: 339-342
    CrossrefPubMedGoogle Scholar
  • 2 Zurawin RK, Dietrich JE, Heard MJ. et al. Didelphic uterus and obstructed hemivagina with renal agenesis: case report and review of the literature. J Pediatr Adolesc Gynecol 2004; 17: 137-141
    CrossrefPubMedGoogle Scholar
  • 3 Purslow CE. A case of unilateral hæmatokolpos, hæmatometra and hæmatosalpinx. BJOG 1922; 29: 643
    CrossrefPubMedGoogle Scholar
  • 4 Herlyn U, Werner H. Simultaneous occurrence of an open Gartner-duct cyst, a homolateral aplasia of the kidney and a double uterus as a typical syndrome of abnormalities. Geburtsh Frauenheilk 1971; 31: 340-347
    PubMedGoogle Scholar
  • 5 Wunderlich M. Unusual form of genital malformation with aplasia of the right kidney. Zentralbl Gynakol 1976; 98: 559-562
    PubMedGoogle Scholar
  • 6 Zhu L, Chen N, Tong JL. et al. New classification of Herlyn-Werner-Wunderlich syndrome. Chin Med J (Engl) 2015; 128: 222-225
    CrossrefPubMedGoogle Scholar
  • 7 Moore KL, Persaud TVN. The developing Human: clinically oriented Embryology. 6th ed. Amsterdam: Saunders; 1998
    Google Scholar
  • 8 Burgis J. Obstructive Müllerian anomalies: case report, diagnosis, and management. Am J Obstet Gynecol 2001; 185: 338-344
    CrossrefPubMedGoogle Scholar
  • 9 Candiani GB, Fedele L, Candiani M. Double uterus, blind hemivagina, and ipsilateral renal agenesis: 36 cases and long-term follow-up. Obstet Gynecol 1997; 90: 26-32
    CrossrefPubMedGoogle Scholar
  • 10 Vercellini P, Daguati R, Somigliana E. et al. Asymmetric lateral distribution of obstructed hemivagina and renal agenesis in women with uterus didelphys: institutional case series and a systematic literature review. Fertil Steril 2007; 87: 719-724
    CrossrefPubMedGoogle Scholar
  • 11 Christianson MS, Yates MM, Woo I. et al. Obstructed hemivagina and ipsilateral renal anomaly (OHVIRA): diagnostic features and management of a frequently misdiagnosed syndrome. Fertil Steril 2012; 98: S222 10.1016/j.fertnstert.2012.07.806
    CrossrefPubMedGoogle Scholar
  • 12 Tong J, Zhu L, Chen N. et al. Endometriosis in association with Herlyn-Werner-Wunderlich syndrome. Fertil Steril 2014; 102: 790-794
    CrossrefPubMedGoogle Scholar
  • 13 Orazi C, Lucchetti MC, Schingo PMS. et al. Herlyn-Werner-Wunderlich syndrome: uterus didelphys, blind hemivagina and ipsilateral renal agenesis. Sonographic and MR findings in 11 cases. Pediatr Radiol 2007; 37: 657-665
    CrossrefPubMedGoogle Scholar
  • 14 Haddad B, Barranger E, Paniel BJ. Blind hemivagina: long-term follow-up and reproductive performance in 42 cases. Hum Reprod 1999; 14: 1962-1964
    CrossrefPubMedGoogle Scholar
  • 15 Tong J, Zhu L, Lang J. Clinical characteristics of 70 patients with Herlyn-Werner-Wunderlich syndrome. Int J Gynaecol Obstet 2013; 121: 173-175
    CrossrefPubMedGoogle Scholar