Download PDF
Open Access
CC BY 4.0 · Indian J Med Paediatr Oncol
DOI: 10.1055/s-0044-1790520
Case Report with Review of Literature

Pediatric Scapular Cavernous Hemangioma Presenting with Kasabach–Merritt Syndrome and Controlled by Preoperative Angioembolization: A Case Report

Authors

  • Pooja Pande 

    1   Department of Radiodiagnosis, Homi Bhabha Cancer Hospital, Tata Memorial Center, Varanasi, Uttar Pradesh, India

  • Suraj Bhame

    1   Department of Radiodiagnosis, Homi Bhabha Cancer Hospital, Tata Memorial Center, Varanasi, Uttar Pradesh, India

  • Harshit Bansal

    1   Department of Radiodiagnosis, Homi Bhabha Cancer Hospital, Tata Memorial Center, Varanasi, Uttar Pradesh, India

  • Raghwesh Ranjan

    2   Division of Pediatric Oncology, Department of Medical Oncology, Homi Bhabha Cancer Hospital, Tata Memorial Center, Varanasi, Uttar Pradesh, India

  • Soumitra Saha

    3   Division of Paediatric Surgical Oncology, Department of Surgical Oncology, Homi Bhabha Cancer Hospital, Tata Memorial Center, Varanasi, Uttar Pradesh, India
Further Information
Also available at
  Permissions and Reprints
Preview

Abstract

Intraosseous hemangioma is a common and benign vascular tumor with a propensity to occur in any bone of the body. Although the most common skeletal sites are the craniofacial bones and the spine, hemangioma of the scapula is a rare occurrence, which is rarer in the pediatric population. Kasabach–Merritt syndrome (KMS) is characterized by the combination of a rapidly growing vascular tumor, thrombocytopenia, microangiopathic hemolytic anemia, and consumptive coagulopathy. This condition can cause massive bleeding even after minor trauma and immediate operative management is usually contraindicated.

We report a rare case of KMS in an 8-year-old girl with cavernous hemangioma of the scapula presenting with progressively increasing shoulder mass, thrombocytopenia, and serially falling hemoglobin levels. She was treated with preoperative angioembolization to manage the consumptive coagulopathy followed by surgery poststabilization. Intraosseous hemangiomas, while benign, can show aggressive features on imaging and angioembolization can be a life-saving tool in the management of vascular tumors presenting with consumptive coagulopathy. Intraosseous hemangiomas, while benign, can show aggressive features on imaging and angioembolization can be a life-saving tool in the management of vascular tumors presenting with consumptive coagulopathy.

Keywords

hemangioma - pediatric - scapula - angioembolization - Kasabach–Merritt - intraosseous

Declaration of the Patient Consent Form

Declared and attached.




Publication History

Article published online:
12 September 2024

© 2024. The Author(s). This is an open access article published by Thieme under the terms of the Creative Commons Attribution License, permitting unrestricted use, distribution, and reproduction so long as the original work is properly cited. (https://creativecommons.org/licenses/by/4.0/)

Thieme Medical and Scientific Publishers Pvt. Ltd.
A-12, 2nd Floor, Sector 2, Noida-201301 UP, India