Beyond the Bone: A Case Report and Review of Literature of Extraskeletal Chondroblastic Osteosarcoma of the Scalp

Abstract

Extraskeletal osteosarcoma (EOS) of the scalp is an extremely rare malignant mesenchymal tumor that accounts for approximately 1 to 2% of all soft tissue sarcoma and 2 to 4% of all osteosarcoma. A 40-year-old man presented with painless swelling on the left side of the scalp for 3 months and right-side limb weakness for 10 days. The patient underwent surgery and the postoperative histopathology report was suggestive of chondroblastic osteosarcoma of the scalp. The patient received five cycles of Adriamycin-based systemic therapy. A response assessment imaging was done, which was suggestive of partial response. Osteosarcoma is chemotherapy- and radiotherapy-resistant tumor; hence, it requires a combined modality approach. Complete surgical excision with adequate surgical margin followed by adjuvant chemotherapy and radiation therapy proved to be one of the optimal treatment modalities.

Keywords

extraskeletal osteosarcoma - chondroblastic osteosarcoma - soft tissue sarcoma

Patient Consent

Written informed consent was given by the attendant for treatment and the prognosis was explained.

Authors' Contributions

J.K. and V.Y. conceived the idea of treatment. All data acquisition was done by A.J.D., N.R., and A.A. Drafting was done by A.J.D. and N.R. All the authors read and approved the final version of the manuscript. *Being a novel case, all the authors have contributed in the decision-making, treatment, and drafting of the report.

Publikationsverlauf

Artikel online veröffentlicht:
20. Februar 2025

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