Onerous Concomitant Complications of Ulcerative Colitis: A Case Report

Zusammenfassung

Ulzerative Kolitis ist eine chronische Entzündung des Kolons, gekennzeichnet durch zeitweilige Exazerbation und Remission. Es kann durch Darmkrebs oder durch eine autoimmun bedingte, extraintestinale Manifestation erschwert werden. Wir stellen hier das Krankheitsbild einer Frau mit ulzerativer Kolitis dar, die die folgenden Krankheiten entwickelte: Sarkoidose, Darmkrebs, primär sklerosierende Cholangitis (PSC) und Gallengangskarzinom. Unserem Wissen nach wurden diese Symptome bisher noch nie bei einem Patienten in solch einer Kombination festgestellt.

Abstract

Ulcerative colitis is a chronic inflammatory disease of the colon characterized by intermittent exacerbations and remissions. It may be complicated with colon cancer or autoimmune-related extracolonic problems. Herein, we present a woman with ulcerative colitis who developed sarcoidosis, colon cancer, primary sclerosing cholangitis, and cholangiocarcinoma. To our knowledge, such associations in a patient have not been reported before.

Schlüsselwörter

ulzerative Kolitis - entzündliche Darmerkrankung - primär sklerosierende Cholangitis - Kolonkrebs - Gallengangkarzinom - malignes Cholangiom - Sarkoidose

Key words

autoimmune disease - ulcerative colitis - inflammatory bowel disease - primary sclerosing cholangitis - colon cancer - bile duct carcinoma - cholangiocarcinoma - sarcoidosis

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