Summary
Fourteen patients with double-chambered right ventricle underwent surgical treatment
and repair of associated anomalies. The anomalous muscle band was isolated in 5 cases,
associated with membranous ventricular septal defect in 7, with discrete sub-aortic
stenosis in one and with double outlet light ventricle in one. All patients survived.
The obstructing muscular band was a hypertrophic structure identifiable either with
a displaced moderator band, still related to the anterior papillary muscle, or with
a giant septoparietal band, inserting to the anterior free wall and occasionally present
in normal hearts. According to this interpretation, referring the obstructive band
to the septomarginal complex, double-chambered right ventricle should not be regarded
strictly as a truncoconal malformation.
Key words
Double-chamber right ventricle - Anomalous muscle bundle of the right ventricle -
Anomalous moderator band - Muscular sub-pulmonary obstruction
