Purpura Schoenlein-Henoch - Ergebnisse der Wörlitzer Konsensusgespräche 2005 zum diagnostischen und therapeutischen Vorgehen

Zusammenfassung

Die Purpura Schoenlein-Henoch (PSH) ist die häufigste Vaskulitis des Klein- und Schulkindes. Die typischen Manifestationen betreffen die Haut, den Gastrointestinaltrakt sowie die Gelenke. Die ebenfalls häufig vorkommende renale Beteiligung ist meist milde und führt nur selten zu einer prognostisch ungünstigen PSH-Nephritis. Trotz der relativen Häufigkeit der Erkrankung stehen für das diagnostische und therapeutische Vorgehen bislang keine Empfehlungen zur Verfügung. Im Rahmen der 8. Konsensusgespräche in Wörlitz im Herbst 2005 wurden Empfehlungen diskutiert und in dieser Arbeit zusammengefasst.

Abstract

Henoch-Schoenlein Purpura (PSH) is the most frequent vasculitis in childhood. Skin, bowel and joints are characteristically involved. Although renal manifestations are common PSH-nephritis is infrequent but characterized by a poor prognosis. In autumn 2005 diagnosis and treatment were discussed at the 8^th consensus meeting in Wörlitz. These results are summarized.

Schlüsselwörter

Purpura - Schoenlein-Henoch - Diagnose - Therapie

Key words

purpura - Schoenlein-Henoch - diagnosis - therapy

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