Download PDF
Neuropediatrics 1985; 16(1): 39-42
DOI: 10.1055/s-2008-1052542
© Georg Thieme Verlag KG Stuttgart · New York

Pseudomonoventricle Due to a Malformation of the Septum Pellucidum

B. T. Poll-The1 , J.  Aicardi2
  • 1Department of Pediatrics, Neuropediatric Division, Free University Hospital Amsterdam, de Boelelaan 1117, 1081 HV Amsterdam, The Netherlands
  • 2Clinique de Génétique Médicale and Inserm U12, Hôpital des Enfants Malades, 149 rue de Sèvres, F-75743 Paris, Cedex 15, France
Further Information

Publication History

Publication Date:
30 April 2008 (online)

  PDF Download  Permissions and Reprints

Abstract

Three children with complete absence of the frontal horns of the lateral ventricles and a single midline cavity on CT scan are reported. Two patients presented with adipsia, persistent serum hyperosmolarity and partial central diabetes insipidus. Another presented with congenital hemiplegia. The CT appearance was different from that of the known causes of monoventricle and was attributable to a malformation of the septum pellucidum, first described neuropathologically by Gross and Kaltenbäck (1957) who termed it frontal pseudomonoventricle.

Key words

Brain malformation - Single cerebral ventricle

      >