Case Report: Macrodystrophia lipomatosa - Illustration of two cases

V Singla; V Virmani; P Tuli; P Singh; N Khandelwal

doi:10.4103/0971-3026.43844

Indian Journal of Radiology and Imaging, Table of Contents

CC BY-NC-ND 4.0 · Indian J Radiol Imaging 2008; 18(04): 298-301
DOI: 10.4103/0971-3026.43844

Musculoskeletal Radiology

Case Report: Macrodystrophia lipomatosa - Illustration of two cases

Authors

V Singla

Department of Radiodiagnosis, Postgraduate Institute of Medical Education and Research, Chandigarh, India
V Virmani

Department of Radiodiagnosis, Postgraduate Institute of Medical Education and Research, Chandigarh, India
P Tuli

Department of Plastic surgery, Postgraduate Institute of Medical Education and Research, Chandigarh, India
P Singh

Department of Radiodiagnosis, Postgraduate Institute of Medical Education and Research, Chandigarh, India
N Khandelwal

Department of Radiodiagnosis, Postgraduate Institute of Medical Education and Research, Chandigarh, India

Abstract

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Abstract

Macrodystrophia lipomatosa is a rare cause of congenital macrodactyly, characterized by progressive proliferation of all mesenchymal elements, with a disproportionate increase in fibroadipose tissue. This developmental anomaly is reportedly more common in the foot than in the hand, with a predilection for the plantar and median nerve distribution. We present two cases of MDL of the hand, one of which had an unusual nerve territory distribution, making clinical diagnosis difficult. Preoperative diagnosis was however made on the basis of radiography and MRI and was later confirmed on surgery.

Keywords

Macrodystrophia lipomatosa - macrodactyly - imaging

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References

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