Melorheostosis with renal arterio-venous malformation: A case report with review of literature

Abdul Rashid Lone; Mushtaq Ahmad; Sheikh Aejaz Aziz; Gul Mohammad Bhat; Javid Rasool Bhat; Rifat Jahan; Shoukat H Khan

doi:10.4103/0971-5851.56336

Indian Journal of Medical and Paediatric Oncology, Inhaltsverzeichnis

CC BY-NC-ND 4.0 · Indian J Med Paediatr Oncol 2009; 30(01): 39-42
DOI: 10.4103/0971-5851.56336

CASE REPORT

Melorheostosis with renal arterio-venous malformation: A case report with review of literature

Authors

Abdul Rashid Lone

Department of Medical Oncology, RCC, Sheri Kashmir Institute of Medical Sciences, Srinagar, Kashmir, India
Mushtaq Ahmad

Department of Medical Oncology, RCC, Sheri Kashmir Institute of Medical Sciences, Srinagar, Kashmir, India
Sheikh Aejaz Aziz

Department of Medical Oncology, RCC, Sheri Kashmir Institute of Medical Sciences, Srinagar, Kashmir, India
Gul Mohammad Bhat

Department of Medical Oncology, RCC, Sheri Kashmir Institute of Medical Sciences, Srinagar, Kashmir, India
Javid Rasool Bhat

Department of Clinical Hematology, RCC, Sheri Kashmir Institute of Medical Sciences, Srinagar, Kashmir, India
Rifat Jahan

Department of Medical Oncology, RCC, Sheri Kashmir Institute of Medical Sciences, Srinagar, Kashmir, India
Shoukat H Khan

Department of Nuclear Medicine, RCC, Sheri Kashmir Institute of Medical Sciences, Srinagar, Kashmir, India

Abstract

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Abstract

Melorheostosis, also known as Leri′s disease and flowing periosteal hyperostosis, is a rare cause of pain and stiffness in a limb. The appearance is of "candle greasing" down one side of one or several bones of the body. We describe a case referred to tertiary care center with suspicion of renal cell carcinoma with diffuse bone metastasis. After reassessment, the patient was diagnosed melorheostosis with renal AV malformation. He was reassured about the benign nature of the disease and is asymptomatic.

Keywords

Flowing periosteal hyperostosis - Leri′s disease - melorheostosis - renal AV malformation

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Referenzen

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