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CC BY-NC-ND 4.0 · J Lab Physicians 2011; 3(01): 056-058
DOI: 10.4103/0974-2727.78571
Case Report

Epignathus with Fetiform Features

Kumar Sunil Y.
Department of Pathology , KS Hegde Medical Academy, Deralakatte, Mangalore, India
,
Shrikrishna U.
Department of Radiology, KS Hegde Medical Academy, Deralakatte, Mangalore, India
,
Jayaprakash Shetty
Department of Pathology , KS Hegde Medical Academy, Deralakatte, Mangalore, India
,
Aishwarya Sitaram
Department of Pathology , KS Hegde Medical Academy, Deralakatte, Mangalore, India
› Author Affiliations Source of Support: Nil
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ABSTRACT

Epignathus is an extremely rare oropharyngeal teratoma that commonly arises from the palate, leading to a high mortality (80-100%) due to airway obstruction in the neonatal period. We present a case of epignathus immature teratoma with fetiform features, originating from basisphenoid in a 28-week preterm male baby, who succumbed to death immediately after birth. Since epignathus is a life-threatening condition at the time of delivery, a prenatal diagnosis is essential to coordinate the treatment and appropriate management by securing the airway, either by endotracheal intubation or tracheostomy followed by complete resection of the tumor.

Keywords

Epignathus - fetiform - immature teratoma - resection


Publication History

Article published online:
29 January 2020

© 2011.

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  • REFERENCES

  • 1 SC Too, Ahmad Sarji S, Syi Yik, TM Ramanujam. Malignant epignathus teratoma. Biomed Imaging Interv J 2008;4:18.
  • 2 Vandenhaute B, Leteurtre, Leconte-Houche M, Pallerin P, Nayts JP, Luisset JM, et al. Epignathus teratoma: Report of three cases with a review of the literature. Cleft Palate-Craniofacial J 2000;37:83-91.
  • 3 Kumar B, Shyam BS. Neonatal oral tumors: Congenital epulis and epignathus. J Pediatr Surg 2008;43:9-11.
  • 4 Lionel J, Valvodo M, Hadi K, Abdul A. Giant epignathus-A case report. Kuwait Med J 2004;36:217-20.
  • 5 Prevedello MD, Kassam BA, Carrau LR, Snyderman HC, Thomas A,Garner P. Transpalatal endoscopic endonasal resection of a giant epignathus skull base teratoma in a new born. J Neurosurg 2007;107:266-71.
  • 6 Frietas RD, Alonso N, Azzolini TD, Gianini-Romano G, Tolazzi AR, Busato l, et al. Epignathus:Two cases. Br J Oral Maxillofac Surg 2008;46:317-9.
  • 7 Holmegren G, Rydnert J. Male fetus with epignathus originating from the ethmoidal sinus. Eur J Obstet Gynecol Reprod Biol 1987;24:69-72.
  • 8 Sanchez AV, Moreno HC, Salfado AS, Serena JC, Irra EJ, Sanchez PG, et al. Epignathus. Cleft Palate Craniofac J 2000;37:83-91.
  • 9 Peter WC. Ultrasonography in obstetrics and gynaecology. 4th ed, Philadelphia: Saunders-An imprint of Elsievier; 2000. p. 316-38.
  • 10 Rumack MC, Wilson RS, Charboneau WJ. Diagnostic ultrasound. 3rd ed, Vol. 2. Netherlands:Mosby- An imprint of Elsievier; 2009. P. 1225-6.
  • 11 Johnston JM, Vyas NA, Kane AA, Molter DW, Smyth MD. Giant intracranial teratoma with epignathus in a neonate:Case report and review of literature. J Neurosurg 2007;106:232-6.
  • 12 Okafor CI, Okafor CO, Odike MA. Congenital teratoma of the face. J Obstetric Gynaecol 2004;24:828-9.
  • 13 Zakaria MA. Epignathus (congenital teratoma of the hard palate): A case report. Br J Oral Maxillofac Surg 1986;24:272-6.
  • 14 Becker S, Schon R, Gutwald R, Otten JE, Maier W, Hentschel R, et al. A congenital teratoma with a cleft palate. Report of a case. Br J Oral Maxillofac Surg 2007;45:326-7.
  • 15 Chattopadhyay A, Patra R, Kumar V. Oral tumors in newborn. India J Pediatr 2003;70:587-8.