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CC BY-NC-ND 4.0 · Avicenna J Med 2014; 04(02): 48-50
DOI: 10.4103/2231-0770.130347
CASE REPORT

A concurrent episode of two neoplasms in a toddler-age child

Muaz A Alrazzak
Department of Pediatrics, Roswell Park Cancer Institute, Buffalo, New York, United States
,
Jenny ZablahAlabi
Department of Pediatrics, Miami Children′s Hospital, Miami, Florida, United States
,
Baraa Alrazzak
Department of Pediatrics, Marshall University, Huntington, West Virginia, United States
,
Guillermo De Angulo
Department of Pediatrics, Miami Children′s Hospital, Miami, Florida, United States
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Abstract

Childhood neoplasms are relatively rare and represent only about 1- 2% of the total incidence of neoplasms in United States. Concurrent episode of childhood cancer is uncommon and usually related to a cancer genetic syndrome. Li Fraumeni Syndrome refers to an autosomal dominant condition that is manifested by the development of certain cancers in early childhood and an increased lifetime risk for developing multiple primary cancers including sarcoma, breast cancer, leukemia, bone cancer, and others. We report a case of a 21-month-old girl who was found to have orbital embryonal rhabdomyosarcoma and adrenocortical tumor concurrently.

Keywords

Adrenocortical tumor - Li Fraumeni syndrome - orbital rhabdomyosarcoma


Publication History

Article published online:
09 August 2021

© 2014. Syrian American Medical Society. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial-License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/).

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