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CC BY-NC-ND 4.0 · Avicenna J Med 2018; 8(03): 110-113
DOI: 10.4103/ajm.AJM_62_18
CASE REPORT

Aggressive orbital rhabdomyosarcoma in adulthood: A case report in a public hospital in Damascus, Syria

Tagrid Younes Ahmad
Department of Internal Medicine, Tishreen hospital, Damascus, Syria
,
Hasan Nabil Al Houri
Department of Internal Medicine, Al Assad University Hospital and Al Mouwasat University Hospital, Damascus, Syria
,
Abdullah Nabil Al Houri
Department of Internal Medicine, University of Jordan, Amman, Syria
,
Nagham Younes Ahmad
Department of Ophthalmology, Yusuf Al-Azma Hospital, Damascus, Syria
› Author Affiliations Financial support and sponsorship Nil.
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Abstract

Orbital rhabdomyosarcoma (RMS) is a highly malignant tumor that originates mainly from mesenchymal tissue. It is considered a rare childhood malignancy; therefore, presentation in adulthood is scarce. In this case report, a 36-year-old male patient presented with a rapidly progressive RMS of the left orbit. The patient was treated in a different institution with radiochemotherapy with good response. However, relapse occurred after 2 months of completing the course, as rapid growing proptosis. Computed tomography scan revealed a lesion in the left orbit with invasion of the left ethmoid cells and the left maxillary sinus. Exenteration of the left orbit with the left partial maxillectomy and ethmoidectomy was performed. RMS is a highly aggressive malignancy that should be considered in any orbital mass that progresses rapidly. Surgery should be the first line in treatment. Delay in diagnosis and inappropriate treatment negatively affects the outcome.

Keywords

Adulthood - oncology - ophthalmology - orbital rhabdomyosarcoma


Publication History

Article published online:
12 August 2021

© 2018. Syrian American Medical Society. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial-License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/).

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