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CC BY-NC-ND 4.0 · Asian J Neurosurg 2020; 15(01): 225-229
DOI: 10.4103/ajns.AJNS_128_19
Case Report

ATRT of lateral ventricle in a child: A rare tumor at a very rare location

Fayçal Lakhdar
Department of Neurosurgery, Hassan II Hospital, University Sidi Mohammed Ben Abdellah, Fez
,
Mohammed Benzagmout
Department of Neurosurgery, Hassan II Hospital, University Sidi Mohammed Ben Abdellah, Fez
,
Yasser Arkha
1   Department of Neurosurgery, Hopital des Spéciaités, University Mohammed V of Medecine, Rabat
,
Khalid Chakour
Department of Neurosurgery, Hassan II Hospital, University Sidi Mohammed Ben Abdellah, Fez
,
Mohammed Chaoui
Department of Neurosurgery, Hassan II Hospital, University Sidi Mohammed Ben Abdellah, Fez
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Atypical teratoid/rhabdoid tumors (AT/RTs) of infancy are highly malignant central nervous system neoplasms that are most commonly seen during the first 2 years of life with limited therapeutic options. To date, only two cases have been described in the lateral ventricle. A 4-year-old boy presented with a 4-month history of increased intracranial pressure. Cerebral magnetic resonance imaging (MRI) revealed a huge intraventricular tumor, occupying the entire temporal horn and the body of the left lateral ventricle. The boy was operated through a left temporal transventricular approach with gross total removal of the lesion. The histopathological diagnosis was an AT/RT. The infant underwent adjuvant chemotherapy and radiation therapy. The 1-year MRI of control showed a local recurrence of the tumor. Then after, Gamma Knife radiosurgery was performed because of the small volume and the deep location of the lesion. At the 3-month follow-up, the MRI showed a significant growth of the tumor volume, and the child was given additional adjuvant chemotherapy. Unfortunately, he died 9 months later. AT/RT of the lateral ventricle is a very rare tumor in children, associated with a poor prognosis in spite of multimodal treatment. Gamma knife surgery (GKS) was rarely reported as a treatment modality of AT/RT. The aim of this work is to discuss about the rarity of this tumor and the best treatment strategy to improve prognosis.

Key-words:

Atypical teratoid/rhabdoid tumor - children - lateral ventricle - radiosurgery - surgery

Financial support and sponsorship

Nil.




Publication History

Received: 05 May 2019

Accepted: 17 September 2019

Article published online:
16 August 2022

© 2020. Asian Congress of Neurological Surgeons. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/)

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