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CC BY-NC-ND 4.0 · Asian J Neurosurg 2019; 14(03): 883-885
DOI: 10.4103/ajns.AJNS_273_17
Case Report

Adult achondroplasia patient with extensive long segment severe C1 to C6 segment spinal canal stenosis: Unique presentation

Guru Satyarthee
Department of Neurosurgery, Neurosciences Centre, AIIMS, New Delhi
,
Kanwaljit Grag
Department of Neurosurgery, Neurosciences Centre, AIIMS, New Delhi
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Achondroplasia represents the common variety of skeletal dysplasia causing short-limb dwarfism. It may be associated with congenial craniovertebral junction anomaly, including atlantoaxial dislocation, Os odointoideum or basilar invagination or acquired as a result of the previous foramen magnum region surgery. However, long segment cervical compression from the first cervical vertebra region to sixth cervical region, such extensive compression producing myelopathy is not reported, and current case represents first case in the western literature. He was managed surgically with a good outcome. Perioperative management along with brief review of pertinent literature along with the management of such case is discussed in brief. Anesthetic management of such patient with coexisting extensive cervical compression presents unique challenges in view of the multisystem involvement along with preexisting anatomical and physiological constraints.

Key-words:

Achondroplasia - anesthesia management - dwarfism - long segment cervical compression - myelopathy

Financial support and sponsorship

Nil.




Publication History

Article published online:
09 September 2022

© 2019. Asian Congress of Neurological Surgeons. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/)

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