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CC BY-NC-ND 4.0 · Asian J Neurosurg 2019; 14(03): 922-926
DOI: 10.4103/ajns.AJNS_59_19
Case Report

Intracranial malignant nerve sheath tumor in the middle cranial fossa: A rare case report with review of literature

Amey Patankar
Department of Neurosurgery, Neuron Hospital, Vadodara, Gujarat
,
Jwalit Sheth
1   Department of Neurosurgery, Neurosurgical Hospital, Vadodara, Gujarat
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Intracranial malignant nerve sheath tumors rarely arise in the central nervous system. They usually arise from the cranial nerves, though rare cases of intraparenchymal lesions have also been reported. We report a case of malignant nerve sheath tumor located in the right middle cranial fossa. Preoperatively, the lesion resembled a meningioma arising from the petrous temporal bone. The lesion was completely excised. Postoperatively, the patient developed righted-sided complete facial nerve palsy. Histopathology and immunohistochemistry revealed the lesion to be a malignant nerve sheath tumor. The development of postoperative facial nerve palsy was puzzling but could be explained if we consider the possibility of the lesion arising from the facial nerve near the geniculate ganglion. Intracranial malignant nerve sheath tumor centered over the geniculate ganglion and projecting into the middle cranial fossa is uncommon, and to the best of our knowledge, only one such case has been previously reported. We review the relevant literature, discuss the management and add to the previously reported cases of this rare condition.

Key-words:

Malignant peripheral nerve sheath tumor - malignant intracerebral nerve sheath tumor - malignant neurofibroma - malignant peripheral nerve sheath tumor - malignant Schwannoma

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Publication History

Article published online:
09 September 2022

© 2019. Asian Congress of Neurological Surgeons. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/)

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