Abstract
Primary renal sarcomas are extremely rare neoplasms accounting for about 1% of all
malignant renal neoplasms. Among all the sarcomas of kidney, leiomyosarcoma is the
most common histotype. The histogenesis of these tumors is unclear, and presumably,
they arise either from renal capsule or smooth muscle of renal vessels or renal pelvis.
We report a case of a 65-year-old woman, who presented with intermittent abdominal
pain for 1 year. The correct diagnosis was established only after the histopathological
analysis of the resected specimen. The poor prognosis borne by these tumors mandates
a thorough evaluation of all renal masses with unusual gross and histomorphology.
Keywords
Leiomyosarcoma - primary - prognosis - renal - vein
