Ewing’s Sarcoma of the Vulva: An Uncommon Tumor in an Uncommon Site

Introduction

Extraskeletal Ewing's sarcoma (EES) is an uncommon, aggressive, round cell tumor. It accounts to 16% among Ewing's sarcoma (ES). The most commonly involved sites are soft tissues of trunk or lower extremities, paravertebral tissues, chest wall, and retroperitoneum. EES presenting in the genitourinary tract is highly uncommon. There are very few cases of primary vulvar and vaginal ES which have been published to date. We report a rare case of ES of the vulva that presented with labial swelling.

Publication History

Received: 12 February 2020

Accepted: 01 May 2020

Article published online:
28 June 2021

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