Solid Pseudopapillary Tumor of Pancreas: A Case Report and Review of Literature

Gursev Sandlas; Charu Tiwari

doi:10.4103/ijmpo.ijmpo_59_16

Indian Journal of Medical and Paediatric Oncology, Table of Contents

CC BY-NC-ND 4.0 · Indian J Med Paediatr Oncol 2017; 38(02): 207-209
DOI: 10.4103/ijmpo.ijmpo_59_16

Case Report

Solid Pseudopapillary Tumor of Pancreas: A Case Report and Review of Literature

Authors

Gursev Sandlas

Department of Paediatric Surgery, Kokilaben Dhirubhai Ambani Hospital, Mumbai, Maharashtra, India
Charu Tiwari

Department of Paediatric Surgery, TNMC and BYL Nair Hospital, Mumbai, Maharashtra, India

Abstract

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Abstract

Solid pseudopapillary neoplasm of the pancreas is one of the rarest forms of pancreatic neoplasm. It was also known as Franz's tumor or Hamoudi tumor until WHO labeled it as solid pseudopapillary tumor (SPT) in 1996. It typically affects young non-Caucasian females in their second or third decade of life. Treatment involves complete excision of the tumor which results in complete cure in majority of the cases. We present here a report of 11-year-old girl with SPT and also do a review of literature for this rare tumor.

Keywords

Children - Franz's tumour - solid pseudopapillary tumor

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References

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