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CC BY-NC-ND 4.0 · Indian J Med Paediatr Oncol 2017; 38(02): 232-235
DOI: 10.4103/ijmpo.ijmpo_5_17
Case Report

Primary Intraosseous Malignant Peripheral Nerve Sheath Tumor of Metacarpal Bones of the Hand in a Patient Without Neurofibromatosis 1: Report of a Rare Case

Bharti Devnani
Department of Radiotherapy and Oncology, AllInstitute of Medical Sciences, New Delhi, India
,
Ahitagni Biswas
Department of Radiotherapy and Oncology, AllInstitute of Medical Sciences, New Delhi, India
,
Sameer Bakhshi
Department of Medical Oncology, AllInstitute of Medical Sciences, New Delhi, India
,
Shah Alam Khan
Department of Orthopedics, AllInstitute of Medical Sciences, New Delhi, India
,
Asit Ranjan Mridha
Department of Pathology, AllInstitute of Medical Sciences, New Delhi, India
,
Shipra Agarwal
Department of Pathology, AllInstitute of Medical Sciences, New Delhi, India
› Author Affiliations Financial support and sponsorship Nil.
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Abstract

Malignant peripheral nerve sheath tumor (MPNST) usually arises in peripheral nerve sheath cells. The intraosseous location of MPNST is rare. Mandible is the most common site of bony involvement. Involvement of bones of the hand is quite unusual. We report a case of MPNST involving metacarpal bones of the left hand treated with surgery followed by adjuvant radiation and chemotherapy and review the pertinent literature.

Keywords

Bone - malignant peripheral nerve sheath tumor - metacarpal - radiotherapy


Publication History

Article published online:
06 July 2021

© 2017. Indian Society of Medical and Paediatric Oncology. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial-License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/.)

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