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CC BY-NC-ND 4.0 · Indian J Med Paediatr Oncol 2020; 41(05): 745-747
DOI: 10.4103/ijmpo.ijmpo_85_20
Case Report and Review of Literature

Long-term Remission of Metastatic Pleomorphic Paratesticular Rhabdomyosarcoma with Chemotherapy in an Adolescent Boy - A Case Report

Intezar Mehdi
1   Department of Pediatric Hematology and Oncology and Bone Marrow Transplantation, Health Care Global, Bengaluru, Karnataka, India
,
Shashi Ranjani
1   Department of Pediatric Hematology and Oncology and Bone Marrow Transplantation, Health Care Global, Bengaluru, Karnataka, India
,
Shivakumar Swamy
2   Department of Radiodiagnosis, Health Care Global, Bengaluru, Karnataka, India
,
K Venkatachala
3   Department of Surgical Oncology, Health Care Global, Bengaluru, Karnataka, India
› Author Affiliations Financial support and sponsorship Nil.
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Abstract

Rhabdomyosarcoma (RMS) is the most common soft tissue sarcoma in the pediatric age group. They are classified based on the histopathological characteristics. The prognosis of RMS depends on the site of occurrence and the histopathology. Although paratesticular site is considered as one of the favorable sites, pleomorphic histology, even at this favorable site, confers a poor prognosis. Treatment includes surgery chemotherapy and radiation in metastatic cases. Here, we describe a case of an adolescent boy with pleomorphic paratesticular RMS treated successfully with chemotherapy.

Keywords

Chemotherapy - pleomorphic - prognosis - rhabdomyosarcoma


Publication History

Received: 27 February 2020

Accepted: 27 May 2020

Article published online:
17 May 2021

© 2020. Indian Society of Medical and Paediatric Oncology. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial-License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/.)

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