Abstract
Posterior reversible encephalopathy syndrome (PRES) is a well-documented pathology
of the brain in systemic upsets. Majority of PRES cases present with edema in the
cerebrum, most commonly in the territory of posterior circulation. It has been reported
to show spinal cord involvement in a rare subgroup known as PRES with spinal cord
involvement (PRES-SCI), with very limited existing literature even in adult patients.
Our institution recently encountered a pediatric case with neurofibromatosis type
I (NF 1) showing PRES with extensive reversible spinal cord changes. This case illustrates
the features of this rare entity in the pediatric group of patients, and is the first
reported case in NF 1 patients.
Keywords
Hypertensive crisis - neurofibromatosis - pediatric posterior reversible encephalopathy
syndrome - posterior reversible encephalopathy syndrome - spinal cord edema