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CC BY-NC-ND 4.0 · Indian J Radiol Imaging 2018; 28(04): 433-435
DOI: 10.4103/ijri.IJRI_489_17
Cardiac

Collateral or fistula? Coronary artery as the primary source of pulmonary blood flow in a patient with pulmonary atresia and ventricular septal defect

Anurag Yadav
Department of Radiodiagnosis, Sir Ganga Ram Hospital, New Delhi, India
,
Salil Bhargava
Department of Radiodiagnosis, Sir Ganga Ram Hospital, New Delhi, India
,
T B S Buxi
Department of Radiodiagnosis, Sir Ganga Ram Hospital, New Delhi, India
,
Krishna Sirvi
Department of Radiodiagnosis, Sir Ganga Ram Hospital, New Delhi, India
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Subject Editor: Financial support and sponsorship Nil.
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Abstract

In patients with pulmonary atresia and ventricular septal defect (PA/VSD), a coronary artery being the primary source of pulmonary blood flow is a rare entity. We describe two cases of PA/VSD with coronary-to-pulmonary artery fistula with emphasis on the role of Computed Tomographic Angiography (CTA) in depicting all the sources of pulmonary blood supply, to predict surgical management and need for unifocalization of Major Aortopulmonary Collateral Arteries (MAPCA’s).

Keywords

Aortopulmonary collateral - coronary artery–pulmonary artery collateral - coronary artery–pulmonary artery fistula - pulmonary atresia - unifocalization - ventricular septal defect


Publication History

Article published online:
26 July 2021

© 2018. Indian Radiological Association. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial-License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/).

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