A 41-year-old man with tetralogy of Fallot and dextrocardia, coronary sinus atrial
septal defect and partially unroofed coronary sinus with persistent left superior
vena cava (PLSVC) underwent a total correction of these anomalies. An association
between these specific anomalies has not been reported previously in the literature.
These defects were successfully corrected by a) closure of the coronary sinus atrial
septal defect with PLSVC entering the right atrium using a pericardial graft; and
b) ventricular partition with a Dacron patch and conotruncal repair for tetralogy
of Fallot. The postoperative course of this patient has been uneventful.
Tetralogy of Fallot - partially unroofed coronary sinus - persistent left superior
vena cava
