Abstract
Colorectal adenomatous polyposis syndromes encompass a diverse group of disorders
with varying modes of inheritance and penetrance. Children may present with overt
disease or within screening programs for families at high risk. We provide an overview
of the array of pediatric polyposis syndromes, current screening recommendations,
and surgical indications and technical considerations. Optimal disease management
for these pediatric patients is still evolving and has implications for screening,
surveillance, pediatric surgical management, and transition of care gastroenterologic
neoplasia physicians and surgeons.
Keywords
IPAA - pediatric polyposis - restorative proctocolectomy
