Variants of Haemophilia B

Susan Elödi; Éva Puskás

doi:10.1055/s-0038-1649033

Thrombosis and Haemostasis, Table of Contents

Thromb Haemost 1972; 28(03): 489-495
DOI: 10.1055/s-0038-1649033

Original Article

Schattauer GmbH

Variants of Haemophilia B

Authors

Susan Elödi

¹Laboratory of Blood Coagulation and Department of Immunochemistry, Central Institute of Haematology and Blood Transfusion, Budapest, Hungary
Éva Puskás

¹Laboratory of Blood Coagulation and Department of Immunochemistry, Central Institute of Haematology and Blood Transfusion, Budapest, Hungary

Abstract

Summary

Variants of haemophilia B were examined by antibody-neutralization technique and by the ox brain thromboplastin time method. On the basis of the presence or absence of anomalous factor IX and of prothrombin time, four variants of haemophilia B were discerned. It is shown that the prolongation of prothrombin time, measured in our cases, cannot be attributed to an inhibitor in the patients’ plasma.

Full Text

References

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