Intralabyrinthine Schwannomas: Disease Presentation, Tumor Management, and Hearing Rehabilitation

Baishakhi Choudhury; Matthew L. Carlson; Daniel Jethanamest

doi:10.1055/s-0039-1678731

Journal of Neurological Surgery Part B: Skull Base, Table of Contents

J Neurol Surg B Skull Base 2019; 80(02): 196-202
DOI: 10.1055/s-0039-1678731

Invited Review

Georg Thieme Verlag KG Stuttgart · New York

Intralabyrinthine Schwannomas: Disease Presentation, Tumor Management, and Hearing Rehabilitation

Baishakhi Choudhury

¹Department of Otolaryngology Head and Neck Surgery, Loma Linda University Health, Loma Linda, California, United States

,

Matthew L. Carlson

²Department of Otorhinolaryngology Head and Neck Surgery, Mayo Clinic, Rochester, Minnesota, United States

,

Daniel Jethanamest

³Department of Otolaryngology Head and Neck Surgery, NYU Langone Health, New York, New York, United States

› Author Affiliations

Abstract

Intralabyrinthine schwannomas (ILS) are rare tumors that frequently cause sensorineural hearing loss. The development and increased use of magnetic resonance imaging in recent years have facilitated the diagnosis of these tumors that present with otherwise nondiscriminant symptoms such as tinnitus, vertigo, and hearing loss. The following is a review of the presentation, pathophysiology, imaging, and treatment with a focused discussion on auditory rehabilitation options of ILS.

Keywords

intralabyrinthine schwannoma - intracochlear schwannoma - intravestibular schwannoma - primary inner ear schwannoma - dizziness - tinnitus - hearing loss - auditory rehabilitation - inner ear masses

Full Text

References

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