Open Access
CC BY-NC-ND 4.0 · Laryngorhinootologie 2019; 98(S 02): S259-S260
DOI: 10.1055/s-0039-1685990
Poster
Oncology

Extrapleural solitary fibrous tumors (SFT) in the ENT field: a Heidelberg case report

Authors

  • SM Friauf

    1   HNO Klinik Universität Heidelberg, Heidelberg

  • M von Winterfeld

    2   Pathologisches Institut Universität Heidelberg, Heidelberg

  • M Praetorius

    1   HNO Klinik Universität Heidelberg, Heidelberg
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    Introduction:

    SFT are rare and potentially malignant vascular tumors. These tumors are slowly progressive and described as indolent swellings. Diagnosis is based upon imaging and histopathologic findings. After histopathologic confirmation, therapy consists of surgical removal and adjunctive radiotherapy if applicable. Even after decades recurrence and metastasis can occur, therefore a life-long follow-up is necessary.

    Methods:

    We present the case of a 71 year old female patient who arrived for the first time in May 2016 with a foreign body sensation in the right eye and diplopia. Clinical examination revealed swelling of the upper lid, ptosis and lowering of the right eye. MRT showed a 3 × 3x2 mm smooth limited and homogeneously enhancing mass lesion of the right eye socket. A transcutaneous orbitotomy and partial resection of the mass lesion was performed. The most recent MRT scan showed a significant progression in size. It was determined further surgical intervention was necessary.

    Results:

    The sample from 2016 showed a sharp limited neoplasia with ectatic and hyperemic blood vessels. The tumor cells showed a nuclear positivity for STAT6 and a Ki67-proliferation rate of approximately 3%. Mitosis rate per 10 HPF accounted for 1 – 2 without signs of necrosis. These findings suggest a diagnosis of an SFT without explicit signs of malignancy. Similar findings were made from the sample obtained in 2018.

    Conclusion:

    Although the majority of SFT are benign tumors metastasis can occur with an incidence of 20 – 50%. The average 5-year survival rate is approximately 85%. The tumor presented in this case did not show malignancy criteria demonstrated on repeat MRT.


     
    Sara Melissa Friauf
    HNO Klinik Universität Heidelberg,
    Im Neuenheimer Feld 400, 69120
    Heidelberg

    Publikationsverlauf

    Publikationsdatum:
    23. April 2019 (online)

    © 2019. The Author(s). This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial-License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/).

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