Schwangerschaft bei Mukoviszidose – ein Überblick

Zusammenfassung

Die Lebenserwartung von Mukoviszidose-Patienten stieg dank intensiver Forschung und Therapie in den letzten 4 Jahrzehnten vom Vorschulalter auf heute über 40 Jahre. Entsprechend nimmt auch die Anzahl von Schwangerschaften an Mukoviszidose erkrankter Frauen zu. Häufig ist für Betroffene die Einschätzung der Konsequenzen einer Schwangerschaft auf ihre Erkrankung und die Auswirkung ihrer Erkrankung auf das heranwachsende Kind nicht möglich. Die Schwangerschaft einer an Mukoviszidose erkrankten Frau mit schlechter Lungenfunktion, reduziertem BMI und Komorbiditäten zeigt erwartungsgemäß mehr Komplikationen als eine Schwangerschaft von Patientinnen ohne entsprechende Risikofaktoren. Generell sind Verläufe mit bestem Outcome für Mutter und Kind unter exakter Planung und engmaschiger multidisziplinärer Betreuung zu erreichen.

^* Die Autoren Michl und Mues haben gleichen Anteil an der Erstellung des Manuskripts.

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