HEMANGIOPERICYTOMA: CASE REPORT

Female, 50 years old, investigating abdominal mass associated with lower limb edema and weight loss of more than 15%. Imaging exams, abdominal MRI, CT abdomen, pelvis and thorax, USG TV showed large, slightly heterogeneous, hypervascular solid mass, with moderate diffusion restriction and abdominopelvic macrolobular contours measuring about 22×20×13cm, in addition to lymph node enlargement in the mediastinal region and nodule. basal region of the right lung lower lobe measuring 1.4×1.0cm. Colonoscopy and EDA showed no significant changes. Opted for surgical intervention. In the inventory of the cavity, abdominal tumors not adhered to other structures of exophytic growth were found, with areas of necrosis, hypervascularization, vascular pedicles in the mesentery root and abdominal wall. The mass in question was excised without affecting adjacent structures. It evolved favorably in the postoperative period andwas discharged at the 6th postoperative day. During outpatient follow-up, an anatomopathological examination was performed, showing a moderately differentiated mesenchymal neoplasia of spindle and epithelioid cells, compatible with the diagnosis of Hemangiopericytoma, with surgical margins compromised by the disease. During follow-up, MRI showed nodular formations with retrovesical heterogeneous signal in the adnexal region, midline near the umbilical region and multiseptive cystic formation in hepatic segment 6 associated with segment 5 hypovascular nodules. A new surgical intervention was performed only with peritoneal biopsy for carcinomatosis. . Was discharged in the 3rd PO. It evolved in the late postoperative period with intestinal subocclusion and death. Hemangiopericytomas are a rare malignant neoplasm that make up approximately 2% of soft tissue tumors, but difficult to determine due to the difficulty in collecting information. Although the incidence is difficult to measure, they are considered rare and make up only 2% of all soft tissue tumors. It is more common between the 5th and 7th decade of life, but can appear at any age, without gender differentiation. There are no known risk factors. The diagnosis is mainly made by exclusion, but with the advent of immunohistochemistry it became possible to better identify this entity. The treatment is basically surgical. This neoplasm is extremely rare and unfavorable, and your best knowledge may help with similar cases in the future.

 

MissingLinkText

No conflict of interest has been declared by the author(s).

Publication History

Article published online:
23 October 2019