DESMOID TUMOR: CASE REPORT

Introduction: The desmoid tumor originates from the fibroblasts of the muscle-aponeurotic tissues, has a high local growth capacity, causing adjacent organ deformities, pain and eventually organic dysfunction. Goal: Report the case of a woman diagnosed with a retroperitoneum desmoid tumor. Method: This is a qualitative, observational study of a case report referring to a patient treated at the General Surgery Outpatient Clinic of the São Francisco de Assis Hospital Complex, located in Belo Horizonte-MG. Case Report: EADS, female, 40 years old, with left lower back pain radiating to the left lower limb and palpable mass of hardened consistency and adhered to the iliac crest. Colonoscopy was performed, which was incomplete due to significant extrinsic compression with the biopsy showing demoid fibromatosis. Magnetic Resonance Imaging showed expansive, infiltrative, highly aggressive lesion involving several structures. Opted for surgical cytoreduction due to rising painful symptoms. During the surgical procedure, tumors of the abdominal wall invading the left iliac crest and abdominal cavity were identified. The tumor was partially resected to an area of bone invasion that was unresectable. The descending colon, as well as other abdominal organs were free and preserved. The anatomopathological study of the lesion confirmed the desmoid tumor. Discussion: The desmoid tumor accounts for less than 3% of all soft tissue tumors, are mostly slow growing, non-metastatic and locally aggressive. Signs and symptoms depend on tumor location, extent, mass size, and lesion growth rate. Local resection is the treatment of choice. Non-hormonal antiinflammatory drugs and estrogen receptor modulators are considered first line in pharmacological treatment. Conclusion: Abdominal mass has numerous etiologies. The importance of recognizing the characteristics of the desmoid tumor for early diagnosis stands out.

 

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Publikationsverlauf

Artikel online veröffentlicht:
23. Oktober 2019