A rare case: Vena cava inferior agenesis with aberrant hepatic vein in an asymptomatic patient^[*]

Summary

Inferior vena cava agenesis is a rare anomaly in an asymptomatic patient. A 58-year-old female patient with complete absence of the inferior vena cava and aberrant right hepatic vein is presented with radiologic findings. To our best knowledge, such a combination of venous anomalies has not previously been documented in the literature and this is the first case in the literature due to the coincidence of total inferior vena cava agenesis with aberrant hepatic vein.

Zusammenfassung

Die Agenesie der Vena cava inferior ist eine seltene Fehlbildung bei einer asymptomatischen Patientin. Eine 58-jährige Patientin mit vollständigem Fehlen der Vena cava inferior und einer aberranten Vena hepatica dextra stellte sich mit radiologischen Befunden vor. Nach unserer Kenntnis wurde bislang keine derartige Kombination von Venenanomalien in der Literatur beschrieben. Dies ist der erste publizierte Fall zu dem Zusammentreffen einer totalen Agenesie der Vene cava inferior mit einer aberranten Vena hepatica.

Keywords

Multidetector computed tomography - angiography - colour doppler ultrasound - agenesis - inferior vena cava

Schlüsselwörter

MDCT - Angiographie - Farbduplexsonografie - Agenesie - Vena cava inferior

^* This study was presented as an e-poster at the 34^th National Radiology Congress in Antalya-Turkey, on November 2013.

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