Seltene Erkrankungen des Mittelohres und der lateralen
                    Schädelbasis

Nora M. Weiss

doi:10.1055/a-1347-4171

Laryngo-Rhino-Otologie, Table of Contents

CC BY-NC-ND 4.0 · Laryngorhinootologie 2021; 100(S 01): S1-S30
DOI: 10.1055/a-1347-4171

Referat

Seltene Erkrankungen des Mittelohres und der lateralen Schädelbasis

Article in several languages: deutsch | English

Nora M. Weiss

¹Klinik für Hals-Nasen-Ohrenheilkunde, Kopf- und Halschirurgie „Otto Körner“ der Universitätsmedizin Rostock, Deutschland

› Author Affiliations

Abstract

Zusammenfassung

Otalgie, Otorrhoe, Tinnitus und Hörminderung zählen zu den häufigsten ohrbezogenen Symptomen, die zum Aufsuchen eines Hals-Nasen-Ohrenarztes führen. Weiterhin spielen Gleichgewichtsstörungen und Affektionen der Hirnnervenfunktion für eine Konsultation eine Rolle. In großen akademischen Zentren, aber auch in der HNO-ärztlichen Grundversorgung kommt der Erkennung von seltenen Erkrankungen des Mittelohres und der lateralen Schädelbasis eine zentrale Rolle zu, da sie häufig eine interdisziplinäre Zusammenarbeit erfordern um die korrekte Diagnose zu stellen und eine adäquate Behandlung zu initiieren. Die folgende Arbeit gibt einerseits eine Übersicht über seltene Formen von osteologischen, neoplastischen, hämatologischen, autoimmunologischen und infektiologischen Erkrankungen sowie Fehlbildungen, die sich im Mittelohr und der lateralen Schädelbasis manifestieren können, andererseits soll ein Überblick über internistische Erkrankungen gegeben werden, deren Manifestation im Mittelohr selten ist.

Die Kenntnis von seltenen Erkrankungen des Mittelohrs und der Schädelbasis ist für die Qualitätssicherung in der Patientenversorgung und insbesondere auch bei entsprechenden chirurgischen Maßnahmen wesentlich. Insbesondere bei untypischen, komplizierten und langwierigeren Krankheitsverläufen muss an seltene Differenzialdiagnosen gedacht werden.

Schlüsselwörter

Differenzialdiagnose - Otorrhoe - Otalgie - seltene Entität - Manifestation - Otitis media

Full Text

References

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