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CC BY 4.0 · European J Pediatr Surg Rep. 2025; 13(01): e4-e8
DOI: 10.1055/a-2590-6030
Case Report

Rare Case of OHVIRA with Ectopic Inguinal Hemiuterus and Ovary

Stefanie Welke
1   Department of Pediatric Surgery and Pediatric Urology, Municipal Hospital Karlsruhe, Karlsruhe, Germany
,
Ferdinand Kosch
1   Department of Pediatric Surgery and Pediatric Urology, Municipal Hospital Karlsruhe, Karlsruhe, Germany
,
Andreas Müller
2   Department of Obstetrics and Gynecology, Karlsruhe Municipal Hospital, Moltkestrasse, Karlsruhe, Germany
,
Amelie Hufnagel-Schmude
3   Department of Radiology, Institute for Pediatric Radiology, Municipal Hospital Karlsruhe, Karlsruhe, Germany
,
Leonie Rother
1   Department of Pediatric Surgery and Pediatric Urology, Municipal Hospital Karlsruhe, Karlsruhe, Germany
,
Verena Ellerkamp
1   Department of Pediatric Surgery and Pediatric Urology, Municipal Hospital Karlsruhe, Karlsruhe, Germany
4   Department of Pediatric Surgery and Pediatric Urology, Eberhard Karls Universitat Tubingen, Tubingen, Germany
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Funding None.
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Abstract

A 12-year-old girl presented with inguinal swelling and recurrent groin pain since menarche. Ultrasound showed an inguinally located ovary with normal perfusion. Herniorrhaphy revealed an ectopic inguinal left ovary with fallopian tube and atretic hemiuterus and a closed internal inguinal ring. Laparoscopy revealed a right-sided hemiuterus and vaginally palpable cervix, leading to the diagnosis of ectopic OHVIRA syndrome type 1.2. The left hemiuterus was resected and the left ovary was pulled through the inguinal canal into the abdomen. During 12 months of follow-up, the left ovary showed normal perfusion and sonomorphologic appearance, menstrual periods were uneventful.

Keywords

OHVIRA syndrome - hemiuterus - hemivagina - vaginal obstruction

Authors' Contributions

V.E. and S.W. conceptualized the manuscript, reviewed the literature, analyzed data, and made major contribution to the writing of the manuscript. S.W., L.R., A.H.S., F.K., V.E., A.M. performed the clinical examination, surgical treatment, and clinical follow-up. V.E., S.W., and F.K. performed final review and editing of the of the manuscript. All authors have read and approved the final version of the manuscript.


Ethical Approval

Written consent for the publication of this case report was obtained from the patient. Approval for case report by the institutional ethics committee is not required.


Patients' Consent

Written informed consent for the publication of this case report and for the accompanying images was obtained from the patient and her parents.




Publikationsverlauf

Eingereicht: 11. Juni 2024

Angenommen: 24. März 2025

Artikel online veröffentlicht:
08. Mai 2025

© 2025. The Author(s). This is an open access article published by Thieme under the terms of the Creative Commons Attribution License, permitting unrestricted use, distribution, and reproduction so long as the original work is properly cited. (https://creativecommons.org/licenses/by/4.0/)

Georg Thieme Verlag KG
Oswald-Hesse-Straße 50, 70469 Stuttgart, Germany

 

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