Urachal Carcinoid—A New Presentation

Introduction

Carcinoid tumors are APUDomas arising from the cells of the amine precursor uptake and decarboxylation system (APUD).[1] Pediatric carcinoid tumors are often indolent, asymptomatic tumors. They may occur in the gut as well as extra-gastrointestinal sites such as lung, bronchus, mediastinum, thymus, pancreas, and gonads.[2] Herein, we report a case of carcinoid tumor originating in the urachus that was managed successfully by surgery alone.

• References

• 1 Van Gompel JJ, Sippel RS, Warner TF, Chen H. Gastrointestinal carcinoid tumors: factors that predict outcome. World J Surg 2004; 28 (4) 387-392
• 2 Caplin ME, Buscombe JR, Hilson AJ, Jones AL, Watkinson AF, Burroughs AK. Carcinoid tumour. Lancet 1998; 352 (9130) 799-805
• 3 Lizerbram EK, Mahour GH, Gilsanz V. Dual patency of the omphalomesenteric duct and urachus. Pediatr Radiol 1997; 27 (3) 244-246
• 4 Schmittenbecher PP. Carcinoid tumours of the appendix in children—epidemiology, clinical aspects and procedures. Eur J Pediatr Surg 2001; 11 (6) 428
• 5 Yokoyama S, Hayashida Y, Nagahama J , et al. Rhabdomyosarcoma of the urachus. A case report. Acta Cytol 1997; 41 (4, Suppl) 1293-1298
• 6 Clapuyt P, Saint-Martin C, De Batselier P, Brichard B, Wese FX, Gosseye S. Urachal neuroblastoma: first case report. Pediatr Radiol 1999; 29 (5) 320-321
• 7 Pelizzo G, La Riccia A, Bouvier R, Chappuis JP, Franchella A. Carcinoid tumors of the appendix in children. Pediatr Surg Int 2001; 17 (5-6) 399-402
• 8 Cilley RE. Disorders of the umbilicus. In: O'Neill Jr JA, Fonkalsrud EW, Coran AG, , eds. Pediatric Surgery. 6th ed. Philadelphia: Mosby Elservier; 2006: 1148-1149
• 9 Oberg K. Chemotherapy and biotherapy in the treatment of neuroendocrine tumours. Ann Oncol 2001; 12 (Suppl. 02) S111-S114