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AJP Rep 2014; 04(02): e61-e64
DOI: 10.1055/s-0034-1370353
Case Report
Thieme Medical Publishers 333 Seventh Avenue, New York, NY 10001, USA.

Microvillus Inclusion Disease Associated with Necrotizing Enterocolitis in a Premature Infant

Ersin Sayar
1   Department of Pediatric Gastroenterology, Faculty of Medicine, Akdeniz University, Antalya, Turkey
,
Salih Kalay
2   Department of Neonatology, Faculty of Medicine, Akdeniz University, Antalya, Turkey
,
Aygen Yilmaz
1   Department of Pediatric Gastroenterology, Faculty of Medicine, Akdeniz University, Antalya, Turkey
,
Osman Oztekin
2   Department of Neonatology, Faculty of Medicine, Akdeniz University, Antalya, Turkey
,
Ali Islek
1   Department of Pediatric Gastroenterology, Faculty of Medicine, Akdeniz University, Antalya, Turkey
,
Gulsum Ozlem Elpek
3   Department of Pathology, Faculty of Medicine, Akdeniz University, Antalya, Turkey
,
Zuhal Kalay
4   Department of Pediatrics, Faculty of Medicine, Akdeniz University, Antalya, Turkey
,
Gonul Tezel
2   Department of Neonatology, Faculty of Medicine, Akdeniz University, Antalya, Turkey
,
Reha Artan
1   Department of Pediatric Gastroenterology, Faculty of Medicine, Akdeniz University, Antalya, Turkey
› Author Affiliations
Further Information

Publication History

02 October 2013

24 December 2013

Publication Date:
12 May 2014 (online)

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Abstract

Microvillus inclusion disease is one of the congenital diarrheal disorders characterized by the appearance of inclusion bodies on the intestinal epithelium. To date there are a few cases and also a few other associated finding reports related to this life-threatening disease in literature. In this report, we present a premature infant with microvillus inclusion disease that was associated with necrotizing enterocolitis. Thus, we should be aware of the appearance of necrotizing enterocolitis in patients with microvillus inclusion disease, especially when contributing factors are present.

Keywords

microvillus inclusion disease - intractable diarrhea - necrotizing enterocolitis - premature
 

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