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Int Arch Otorhinolaryngol 2015; 19(02): 151-155
DOI: 10.1055/s-0034-1390328
Original Research
Thieme Publicações Ltda Rio de Janeiro, Brazil

Auditory Neuropathy/Dyssynchrony: A Retrospective Analysis of 15 Cases

Murat Unal
1   Department of Otorhinolaryngology, Mersin University, Mersin, Turkey
,
Yusuf Vayisoglu
1   Department of Otorhinolaryngology, Mersin University, Mersin, Turkey
› Author Affiliations
Further Information

Publication History

04 June 2014

25 August 2014

Publication Date:
28 November 2014 (online)

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Abstract

Introduction Auditory neuropathy/dyssynchrony (AN/AD) comprises a spectrum of pathology affecting the auditory pathways anywhere from the inner hair cells to the brainstem. It is characterized by an absent or atypical auditory brainstem response (ABR) with preservation of the cochlear microphonics and/or otoacoustic emissions (OAEs).

Objective Retrospective analysis of patients with AN/AD.

Methods Fifteen patients with AN/AD were included in this study and their records were retrospectively investigated.

Results Possible etiology of AN/AD was neonatal hyperbilirubinemia in three patients, family history of hearing loss in three patients, consanguineous marriage in two patients, head trauma in two patients, mental motor retardation in one patient, cerebrovascular disease in one patient, and there was no apparent cause in three patients.

Conclusion Otolaryngologists should keep in mind the diagnosis of AN/AD especially in patients complaining of difficulty in hearing and speech and audiological evidence of disassociation between pure tone and speech audiometry. ABR and OAE testing is recommended in these patients for AN/AD diagnosis.

Keywords

auditory neuropathy/dyssynchrony - otoacoustic emission - auditory brainstem response
 

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