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Int Arch Otorhinolaryngol 2016; 20(01): 087-092
DOI: 10.1055/s-0034-1544116
Case Report
Thieme Publicações Ltda Rio de Janeiro, Brazil

Aglossia: Case Report

Silvana Bommarito
1   Speach Therapy Department, Universidade Federal de São Paulo, São Paulo, São Paulo, Brazil
,
Luciana Escanoela Zanato
2   Human Health Department, Universidade Nove de Julho, São Paulo, São Paulo, Brazil
,
Marilena Manno Vieira
1   Speach Therapy Department, Universidade Federal de São Paulo, São Paulo, São Paulo, Brazil
,
Fernanda Angelieri
3   Faculdade da Saúde, Universidade Metodista de São Paulo, São Paulo, São Bernardo do Campo, Brazil
› Author Affiliations
Further Information

Publication History

31 October 2014

16 December 2014

Publication Date:
30 January 2015 (online)

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Abstract

Introduction Aglossia is a rare condition caused by failure of the tongue embryogenesis process (in the fourth to eighth weeks of gestation). The tongue is an organ used in different activities such as sucking, swallowing, chewing, and talking. It is also responsible for shaping palate dental arches (in its absence, they become atrophic). There are few similar cases reported in the literature.

Objective To describe a rare case of aglossia and the multidisciplinary professionals working together for 5 years to treat the patient.

Resumed Report An 8-year-old girl with aglossia had an assessment comprising: (1) clinical assessment of the stomatognathic system related to resting posture, tonus, and mobility; (2) orthodontic assessment; (3) surface electromyography of the chewing muscles; (4) swallowing videofluoroscopy.

Conclusion The authors confirmed the need of multidisciplinary cooperation to improve the patient's quality of life, because agenesia implicates many activities/functions that depend on the tongue to fully work. Multiprofessional cooperation helps the patient learn compensation mechanisms.

Keywords

stomatognathic system - tongue - malocclusion - articulation disorders - deglutition disorders
 

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