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CC BY 4.0 · European J Pediatr Surg Rep. 2017; 05(01): e1-e3
DOI: 10.1055/s-0037-1598624
Case Report
Georg Thieme Verlag KG Stuttgart · New York

Discontinued Splenogonadal Fusion and Bilateral Empty Scrotum in an 18-Month-Old Boy

Ahmed Abokrecha
1   Department of Pediatric Surgery, Maternity and Children Hospital, Makkah, Saudi Arabia
,
Ameera Almatrfi
2   Department of Medicine and Surgery, Umm Al-Qura University Faculty of Medicine, Makkah, Saudi Arabia
› Author Affiliations
Further Information

Publication History

16 August 2016

05 January 2017

Publication Date:
02 March 2017 (online)

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Abstract

Splenogonadal fusion is a rare benign congenital anomaly defined as the presence of splenic tissue adherent to gonads. It was first described in 1883 by Bostroem, a German pathologist. We present a case of an 18-month-old boy who was referred as a case of bilateral empty scrotum since birth. During routine laparoscopic exploration, right vas deferens and testicular vessels were entering the right internal inguinal ring so right inguinal exploration was done, which revealed blind ending vas deferens and testicular vessels and the left testis was found intra-abdominally near the left internal ring with a mass on its upper pole. Wedge biopsy was taken from the upper pole of the testicle (site of the mass) for tissue diagnosis followed by orchidopexy. Histology showed splenic tissue. Although splenogonadal fusion is a rare condition, surgeons should be aware of this rare disease entity to avoid unnecessary aggressive interventions such as orchiectomy.

Keywords

Bilateral Empty Scrotum - orchidopexy - discontinued splenogonadal fusion
 

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